Substrate
Lysosomal enzyme
Disease : enzyme deficiency
Muscle
glycogen
Acid Maltase
Pompe
Glucosaminoglycans
(mucopolysaccharides),
essential for collagen tissues
Iduronidase
MPS I/ Hurler/Scheie
Arylsulfatase B
MPS VI/ Maroteaux-Lamy.
+ NH2
+
Ceramide
Glycosylceramides
or glycosphingolipids, essential for cell membranes & nervous system
Galactocerebroside
Alpha galactosidase
Fabry
Glucocerebroside
Beta glucosidase
Gaucher
Hexosamidinase A
Tay Sachs
Acid
Sphingomyelinase

Niemann Pick A & B *
Arylsulfatase A
Metachromatic
leukodystrophy
Iduronate sulfatase
MPS II/ Hunter
SUGAR
More
sugar
Other
glycosphingolipids
&
sphingomyelins
Some lysosomal storage diseases
HealthValue
Gaucher
Lysosomal diseases
Ceramides & Sphingolipids
Biosynthesis of lysosomes
Mannose 6 Phosphate & recognition of lysosomal enzymes
Lysosomes, cellular waste disposal facilities
For more info, click on the underlined links below :
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Alpha mannosidase
Oligosaccharides
* Niemann Pick C & D are linked to deficient trafficking of  exogenous cholesterol towards lysosomes
Alphamannosidosis and its toxic equivalent in grazing animals contaminated by swainsonine
   Cystine
Cystinosis
Lysosomal membrane cystinosine
Take a look at "Miracle in Pompe Disease"
from Malaysia Lysosomal Disease Organisation
Morquio A
Morquio B
Galactose 6 sulfatase
Beta galactosidase